Kasabach-Merrit syndrome in infants


SARIHAN H., MOCAN H., ABEYS M., AKYAZICI R., Cay A. , IMAMOGLU M.

PANMINERVA MEDICA, cilt.40, ss.128-131, 1998 (SCI İndekslerine Giren Dergi) identifier identifier identifier

  • Cilt numarası: 40 Konu: 2
  • Basım Tarihi: 1998
  • Doi Numarası: 10.1016/j.jvir.2015.12.012
  • Dergi Adı: PANMINERVA MEDICA
  • Sayfa Sayısı: ss.128-131

Özet

Methods. Four infants with Kasahach-Merrit syndrome have been treated at the University Hospital, Trabzon. They had large varied-site cutaneous hemangiomas. Diagnosis was performed with clinical and laboratory studies. All patients has severe thombocytopenia and anemia. Fibrinogen and fibrin split products were examined in two patients and lower fibrinogen and over fibrin split products levels were detected in them. All patients were admitted to the intensive care unit and they were treated with antibiotics, fresh blood transfusion and thombocyte suspension. Two out of four patients were previously treated with steroids unsuccessfully and one patient died due to disseminated intravascular coagulopathy, Three patients were treated with interferon alfa-2a and compression.