A case of angioedema-like atypic scleromyxedema responding to treatment with steroid


Polat A., KAPICIOĞLU Y., Sahin N. , Yilmaz M.

TURKDERM-TURKISH ARCHIVES OF DERMATOLOGY AND VENEROLOGY, cilt.50, ss.28-30, 2016 (ESCI İndekslerine Giren Dergi) identifier identifier

  • Cilt numarası: 50 Konu: 1
  • Basım Tarihi: 2016
  • Doi Numarası: 10.4274/turkderm.04809
  • Dergi Adı: TURKDERM-TURKISH ARCHIVES OF DERMATOLOGY AND VENEROLOGY
  • Sayfa Sayıları: ss.28-30

Özet

Lichen myxedematosus is a chronic, inflammatory, systemic dermatose characterized by dermal musin deposition and increased fibroblasts in the absence of thyroid dysfunction. It is usually seen together with paraproteinemia. It is clinically classified as scleromyxedema (papular mucinosis), localized lichen myxedematosus, and atypical lichen myxedematosus. Etiopathogenesis of the disease which is very difficult to treat is still unknown. Herein, we present a case of atypical scleromyxedema without monoclonal gammopathy mimicking angioedema, rapidly developing and responding to steroid treatment.