A rare tumor of craniofacial bones in children: A pediatric chondroblastic osteosarcoma case with diagnostic and therapeutic problems


Uysal K., Koyuncuoglu M., Akman F., Guneri A., Sarialioglu F., Kargi A., ...More

PEDIATRIC HEMATOLOGY AND ONCOLOGY, vol.18, no.2, pp.147-152, 2001 (Journal Indexed in SCI) identifier identifier identifier

  • Publication Type: Article / Article
  • Volume: 18 Issue: 2
  • Publication Date: 2001
  • Doi Number: 10.1080/088800101300002991
  • Title of Journal : PEDIATRIC HEMATOLOGY AND ONCOLOGY
  • Page Numbers: pp.147-152

Abstract

Osteosarcoma of the cranial facial region is uncommon and only rarely involves the ethmoid or sphenoid bones. The authors report on an unusual case of a 17-year-old male presenting with chondroblastic osteosarcoma of the maxillary, ethmoid, and sphenoid sinuses who remains well and disease-free at 46 months. He was treated with anterior craniofacial resection followed by postoperative radiotherapy to the sight of the primary tumor. He did not receive chemotherapy because of emerging hepatitis-B infection and vasculitis. The literature on extragnathic craniofacial osteosarcomas is reviewed with particular emphasis on treatment options of this rare tumor.