Presacral/retroperitoneal schwannomas are extremely unusual and their surgical approach is challenging. Various surgical approaches have been proposed. Here we describe our experience with the anterior extraperitoneal approach for the Type 3 presacral/retroperitoneal schwannoma. A 33-year-old woman presented with a history of infertility and a presacral/retroperitoneal mass. The patient underwent abdominal/pelvic CT and MRI that demonstrated presence of a solid, well circumscribed Type 3 presacral/retroperitoneal schwannoma. The anterior extraperitoneal approach was successfully used to remove the presacral/retroperitoneal schwannoma. The histopathological evaluation confirmed the preoperative diagnosis. The anterior extraperitoneal approach is helpful as an alternative approach in the surgical management of benign Type 3 presacral/retroperitoneal schwannomas (Fig. 4, Ref. 15). Full Text in free PDF www.bmj.sk.