Assessment of Right Heart Functions in Children with Mild Cystic Fibrosis.

Guliyeva A., Cakir E., Yazan H., AlShadfan L., Sharifov R., Temur H., ...More

Klinische Padiatrie, vol.233, no.5, pp.231-236, 2021 (SCI-Expanded) identifier identifier identifier

  • Publication Type: Article / Article
  • Volume: 233 Issue: 5
  • Publication Date: 2021
  • Doi Number: 10.1055/a-1341-1698
  • Journal Name: Klinische Padiatrie
  • Journal Indexes: Science Citation Index Expanded (SCI-EXPANDED), Scopus, CAB Abstracts, EMBASE, MEDLINE
  • Page Numbers: pp.231-236
  • Keywords: Childhood Age Group, Cor Pulmonale, Cystic fibrosis, Pulmonary function test, Pulmonary hypertension
  • Bezmialem Vakıf University Affiliated: Yes


Background Cystic fibrosis (CF) is a multisystemic disease that prevalently involves the lungs. Hypoxemia occurs due to the existing of progressive damage to the pulmonary parenchyma and pulmonary vessels. The condition may cause systolic and diastolic dysfunction to the right ventricle due to the effects of high pulmonary artery systolic pressure (PASP). The study aimed to determine echocardiographic alterations in PASP, right ventricle (RV) anatomy, and functions in mild CF children.