Psychotic disorder in a case with Hallervorden-Spatz disease

ONER O., ONER P., DEDA G., Icagasioglu D. F.

ACTA PSYCHIATRICA SCANDINAVICA, vol.108, no.5, pp.394-397, 2003 (SCI-Expanded) identifier identifier identifier

  • Publication Type: Article / Article
  • Volume: 108 Issue: 5
  • Publication Date: 2003
  • Doi Number: 10.1034/j.1600-0447.2003.00159.x
  • Journal Indexes: Science Citation Index Expanded (SCI-EXPANDED), Social Sciences Citation Index (SSCI), Scopus
  • Page Numbers: pp.394-397
  • Bezmialem Vakıf University Affiliated: No


Objective: Hallervorden - Spatz disease is a rare autosomal recessive condition, with early onset of predominantly extrapyramidal dysfunction. The symptoms of the disease are dystonia, rigidity, choreoathetosis, pyramidal signs, and intellectual decline. Recent genetic studies mapped the disease to chromosome 20p12.3-p13, and identified mutations in the pantothenate kinase gene. This report describes a childhood onset case of Hallervorden - Spatz disease with schizophreniform psychotic symptoms. Former reports about the psychiatric comorbidity generally included depressive disorder.