Emergency Difficult Airway Management in a Patient with Severe Epidermolysis Bullosa


ÖZKAN A. S. , Kayhan G. E. , AKBAŞ S. , Kacmaz O., DURMUŞ M.

TURKISH JOURNAL OF ANAESTHESIOLOGY AND REANIMATION, vol.44, no.5, pp.270-272, 2016 (Journal Indexed in ESCI) identifier identifier identifier

  • Publication Type: Article / Article
  • Volume: 44 Issue: 5
  • Publication Date: 2016
  • Doi Number: 10.5152/tjar.2016.49260
  • Title of Journal : TURKISH JOURNAL OF ANAESTHESIOLOGY AND REANIMATION
  • Page Numbers: pp.270-272
  • Keywords: Epidermolysis bullosa, nasal fiberoptic intubation, difficult airway, DYSTROPHICA

Abstract

Epidermolysis bullosa (EB) is a rare disease characterised by vesiculobullous lesions with minimal trauma to the skin and mucous membranes. Bleeding, scar tissue, contractures, oedema and lesions that can spread throughout the body can cause a difficult airway and vascular access in patients with EB. Therefore, anaesthetic management in patients with EB is a major problem even for experienced anaesthesiologists. Herein, we report a case of difficult airway management in a patient diagnosed with severe EB who presented for emergency tracheostomy because of respiratory failure under general anaesthesia.